STM Article Repository

Desmoplastic infantile ganglioglioma (DIG) is a rare glioneuronal tumor characterized by prominent collagen-rich stroma, spindle cell glial component, and small ganglion cells (WHO grade I). The tumor is more frequently identified in the supratentorial region of patients aged less than 1 year with clinical features of macrocephaly or seizures. DIGs are solid-cystic tumors with sharp demarcation from the brain and/or attached to the dura and are associated with a favorable prognosis after complete surgical resection. In this article, we report a case of DIG in a 4-year-old girl presenting with headache, absence seizures, and decreased muscle tone. No clinical signs of recurrence were observed during 8 months of follow-up.